Calciphylaxis cutis

MedGen UID:: 900547
•Concept ID:: C4274083
•: Disease or Syndrome

Synonym:	calciphylaxis cutis
SNOMED CT:	Calciphylaxis cutis (717043006)

Monarch Initiative:	MONDO:0017216
Orphanet:	ORPHA280065

Definition

A life-threatening syndrome with manifestation of progressive and painful skin ulcerations associated with calcification of medium-size and small cutaneous arterial vessels. It affects mainly patients on dialysis or after renal transplantation. [from SNOMEDCT_US]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVCalciphylaxis cutis

Phenotypic abnormality
- Abnormality of the musculoskeletal system
  - Abnormality of the musculature
    - Abnormal skeletal muscle morphology
      - Calcinosis
        Calciphylaxis
        Calciphylaxis cutis

Professional guidelines

PubMed

Management of Cutaneous Calciphylaxis.

Kodumudi V, Jeha GM, Mydlo N, Kaye AD
Adv Ther 2020 Dec;37(12):4797-4807. Epub 2020 Sep 30 doi: 10.1007/s12325-020-01504-w. PMID: 32997277 Free PMC Article

Calciphylaxis: Approach to Diagnosis and Management.

Seethapathy H, Noureddine L
Adv Chronic Kidney Dis 2019 Nov;26(6):484-490. doi: 10.1053/j.ackd.2019.09.005. PMID: 31831126

Calciphylaxis: Diagnosis, Pathogenesis, and Treatment.

Chang JJ
Adv Skin Wound Care 2019 May;32(5):205-215. doi: 10.1097/01.ASW.0000554443.14002.13. PMID: 31008757

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